Pathways of ammonia detoxification to GLN in muscles associated with Improved use on the BCAA and ?-KG (cataplerosis) and instructed results of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Constructive influence of BCAA on ammonia detoxification to GLN can be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenyl